Congenital Nasal Pyriform Aperture Stenosis Repair: A Case Series and Discussion of Postoperative Care

Authors

Harper L. Wilson, University of KentuckyFollow
Nicholas Van Maele, University of KentuckyFollow
Kenneth C. Iverson, University of KentuckyFollow

Abstract

Congenital nasal pyriform aperture stenosis (CNPAS) is a rare condition related to holoprosencephaly in which bony overgrowth of the medial nasal process of the maxilla narrows the pyriform aperture. CNPAS presents in neonates with signs of upper airway obstruction ranging from mild to severe respiratory distress and failure to thrive. Surgical intervention is indicated after failed conservative measures and generally includes temporary stent placement. We report a series of 3 cases of CNPAS treated surgically, examine postoperative care recommendations in the literature, and present a comprehensive postoperative care regimen with a novel method to maintain stent patency.

Document Type

Article

Publication Date

12-5-2020

Notes/Citation Information

Published in Otolaryngology Case Reports, v. 18, 100247.

© 2020 Elsevier Inc.

This is an open access article under the CC BY-NC-ND license (https://creativecommons.org/licenses/by-nc-nd/4.0/).

Digital Object Identifier (DOI)

https://doi.org/10.1016/j.xocr.2020.100247

Repository Citation

Wilson, Harper L.; Van Maele, Nicholas; and Iverson, Kenneth C., "Congenital Nasal Pyriform Aperture Stenosis Repair: A Case Series and Discussion of Postoperative Care" (2020). Otolaryngology--Head & Neck Surgery Faculty Publications. 12.
https://uknowledge.uky.edu/otolaryngology_facpub/12